|
KMID : 1084220160230010061
|
|
Journal of Rheumatic Diseases
2016 Volume.23 No. 1 p.61 ~ p.65
|
|
|
A Case of Non-Hodgkin’s Lymphoma of the Ocular Adnexa and Lung in a 17-year-old with Primary Sjogren’s Syndrome
|
|
:Kim Sang-Hyun
:Lee Han-Ah/:Park Seung-Woon/:Lee Kang-Won/:Seo Young-Ho/:Kim Jae-Hoon/:Choi Sung-Jae/:Lee Young-Ho/:Ji Jong-Dae/:Song Gwan-Gyu
|
|
|
Abstract
|
|
|
|
Sjogren’s syndrome (SS) is a chronic autoimmune disorder characterized by lymphocyte-mediated destruction of exocrine glands, which produces classical symptoms of dry eyes and dry mouth. Aside from the clinical manifestations associated with exocrine glands, extraglandular features of SS include a major long-term concern for development of lymphoma. The lifetime risk of non-Hodgkin’s lymphoma (NHL) in an SS patient is approximately 5% to 10%, 20 times higher than that of the normal population. This case report describes a rare occurrence of NHL in the eyelid and lung of an adolescent female with SS, whose disease activity had been monitored closely. This is the first reported case in Korea. (J Rheum Dis 2016;23:61-65)
|
|
|
KEYWORD
|
|
|
Sjogren’s syndrome, Lymphoma, Conjunctiva, Lung
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
  
|